This document is the result of an European Consensus conference which took place in
Artimino, Tuscany, Italy, in March 2001 involving 33 experts on nutrition in patients with …

Developments in managing CF continue to drive dramatic improvements in survival. As
newborn screening rolls-out across Europe, CF centres are increasingly caring for cohorts of …

Background Cystic fibrosis transmembrane conductance regulator (CFTR) modulators
correct the basic defect caused by CFTR mutations. Improvements in health outcomes have …

Identifying subjects with cystic fibrosis (CF) who may benefit from cystic fibrosis
transmembrane conductance regulator (CFTR)–modulating drugs is time-consuming, costly …

In vitro drug tests using patient-derived stem cell cultures offer opportunities to individually
select efficacious treatments. Here, we provide a study that demonstrates that in vitro drug …

Recent evidence-based nutritional guidelines and improved medical treatment support the
nutritional monitoring and interventions in CF patients. Nutritional care should be …

The improved survival in people with cystic fibrosis has led to an increasing number of
patients reaching adulthood. This trend is likely to be maintained over the next decades …

Background: Pulmonary administration of colistin is one of the antimicrobial treatments used
in Cystic Fibrosis (CF) patients chronically infected with Pseudomonas aeruginosa. Dry …

Dry powder inhalation of antibiotics in cystic fibrosis (CF) therapy may be a valuable
alternative for wet nebulisation, because it saves time and it improves lung deposition. In this …

BACKGROUND: Dry powder inhalation (DPI) may be an alternative to nebulisation of drugs
in the treatment of chest infections in cystic fibrosis (CF) patients. In a pilot study the …